Primary cutaneous adenoid-cystic carcinoma of thigh found accidentally and presenting with the clinical picture of small pigmented (dark brown) cutaneous fibroma

Strahil Strashilov, Stanislav Slavchev, Vasil Nanev, Denislava Ivanova, Momchil Ivanov, Ivan Ivanov, Angel Yordanov


The primary cutaneous adenoid-cystic carcinoma represents a very rare neoplasm - less than 100 similar cases are reported in the literature until now. It affects persons of middle age or elder the female is involved a little more often the local relapses are observed in about half of the cases and it metastasizes most frequently in the regional lymph nodes and lungs.

We present a case of a 31-year-old woman with primary adenoid-cystic carcinoma of skin which was treated for a pigmented cutaneous fibroma. This required reoperating the patient.

The clinical manifestation of primary cutaneous adenoid-cystic carcinoma may imitate benign pigmented cutaneous fibroma. The final diagnosis of this disease is made by a pathologist based on the pathomorphological exam and immunohistochemistry. The basic method for treatment in these cases is the extensive local excision in a radius of 2cm from the lesion to avoid the risk of local relapse.
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