Background
Schizencephaly is one of the most severe forms of neuronal migration defects and is an extremely rare cause of seizure disorder.

Case details
We report a case of bilateral schizencephaly (Type II) presenting as seizure disorder since birth.

Discussion
This case is rare because of the relatively benign features compared to other reported cases.

Conclusion
Compared to other cases, this patient has normal cognitive and motor functioning. Given the scant literature on schizencephaly in India’s paediatric population, this case highlights the possibility of a very rare entity associated with seizures. MRI can detect this condition.